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Radiologic-Pathologic correlation


Gardner's Syndrome

Sapna PanjwaniAnjana BagewadiVaishali KeluskarSaurabh Arora
Departments of Oral Medicine and Radiology, Conservative Dentistry and Endodontics, Institute of Dental Studies and Technologies, Kadrabad, Modinagar, Ghaziabad, Uttar Pradesh, Oral Medicine and Radiology, Kles V.K Institute of Dental Sciences, Nehru Nagar, Belgaum, Karnataka, India
Date of Submission: 02-Nov-2011, Date of Acceptance: 31-Dec-2011, Date of Web Publication: 31-Dec-2011.
Corresponding Author:
Corresponding Author

Sapna Panjwani

Department of Oral Medicine and Radiology, Institute of Dental Studies and Technologies, Kadrabad, Modinagar, Ghaziabad, Uttar Pradesh, India.
E-mail: dr.sapna28@gmail.com

Corresponding Author:
Corresponding Author

Sapna Panjwani

Department of Oral Medicine and Radiology, Institute of Dental Studies and Technologies, Kadrabad, Modinagar, Ghaziabad, Uttar Pradesh, India.
E-mail: dr.sapna28@gmail.com

DOI: 10.4103/2156-7514.92187 Facebook Twitter Google Linkedin

ABSTRACT


Gardner's syndrome is an autosomal dominant disease and is a subtype of familial adenomatous polyposis. It is characterized by adenomatous intestinal polyps, multiple osteomas in the skull, maxillae, mandible, and multiple cutaneous and subcutaneous masses (epidermoids and desmoid). Intestinal polyps, if not treated, have 100% chance of becoming malignant. We report a case of a 25-year-old female patient with Gardner's syndrome, with clinical manifestations including impacted supernumerary teeth, odontomes, sebaceous cyst on the scalp, and osteomas. It is important for the general dental practitioners to be aware of the clinical and radiological characteristics of Gardner's syndrome.
Keywords: Familial Intestinal Polyposis, Gardner's Syndrome, Impacted Teeth, Osteoma

Cited in 17 Documents

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