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Case report

Quadricuspid Aortic Valve: A Rare Congenital Cause of Aortic Insufficiency

Rahul Vasudev1Priyank Shah2Mahesh Bikkina2Fayez Shamoon2
1Departments of Internal Medicine and, 2Cardiology, St. Joseph’s Regional Medical Center, 07503 NJ, USA
Date of Submission: 15-Feb-2016, Date of Acceptance: 18-Mar-2016, Date of Web Publication: 30-Mar-2016.
Corresponding Author:

Rahul Vasudev

E-mail: drrahulvasudev@gmail.com

Corresponding Author:

Rahul Vasudev

E-mail: drrahulvasudev@gmail.com

DOI: 10.4103/2156-7514.179417 Facebook Twitter Google Linkedin


Quadricuspid aortic valve (QAV) is a rare congenital cardiac anomaly causing aortic regurgitation usually in the fifth to sixth decade of life. Earlier, the diagnosis was mostly during postmortem or intraoperative, but now with the advent of better imaging techniques such as transthoracic echocardiography, transesophageal echocardiography (TEE), and cardiac magnetic resonance imaging, more cases are being diagnosed in asymptomatic patients. We present a case of a 39-year-old male who was found to have QAV, with the help of TEE, while undergoing evaluation for a diastolic murmur. The patient was found to have Type B QAV with moderate aortic regurgitation. We also present a brief review of classification, pathophysiology, and embryological basis of this rare congenital anomaly. The importance of diagnosing QAV lies in the fact that majority of these patients will require surgery for aortic regurgitation and close follow-up so that aortic valve replacement/repair is done before the left ventricular decompensation occurs.
Keywords: Aortic regurgitation, congenital valvular diseases, quadricuspid aortic valve, transesophageal echocardiography quadricuspid valves

Cited in 5 Documents

  1. Nicholas Suraci, Sofia A. Horvath, Daniela Urina, Gerald Rosen and Orlando Santana (2019) Quadricuspid aortic valve: Case series and review of literature. Echocardiography 36(2):406. doi: 10.1111/echo.14240
  2. Yi Lin, Kanhua Yin, Yulin Wang, Danjuan Yang, Rongkui Luo, Lili Dong, Zhiqi Zhang and Chunsheng Wang (2018) Clinical characteristics and surgical outcomes of dysfunctional quadricuspid aortic valve. Journal of Surgical Research 229:223. doi: 10.1016/j.jss.2018.04.003
  3. V. Chetboul and C. Taton (2018) Encyclopédie Animée D'imagerie Cardiovasculaire Ultrasonore du Chien et du Chat. 387. doi: 10.1016/B978-2-294-74873-8.00009-6
  4. Hassan Tatari, Maziar Gholampour Dehaki, Gholamreza Omrani, Hafez Ghaheri, Alwaleed Al-Dairy and Hojjat Mortezaeian (2018) Intraoperative diagnosis of a quadricuspid aortic valve. Asian Cardiovasc Thorac Ann 26(9):704. doi: 10.1177/0218492317692467
  5. Christopher Jackson, Tahira Sarwar, Inyong Hwang, Kiran Joglekar and Shadwan Alsafwah (2018) Quadricuspid aortic valve infective endocarditis. J Clin Ultrasound 46(2):145. doi: 10.1002/jcu.22495

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