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Review article


Dermatofibrosarcoma Protuberans: Insights into a Rare Soft Tissue Tumor

Aliya Sarhan Al BarwaniSawsan TaifReem Ahmed Al MazrouaiKhamis Salim Al MuzahmiAsif Alrawi
Department of Radiology, Khoula Hospital, MuscatOman Medical Speciality Board, Radiology Training Program,Sultanate of OmanThe James Cook University Hospital, South Tees Hospitals NHS, UK
Date of Submission: 10-Mar-2016, Date of Acceptance: 14-Apr-2016, Date of Web Publication: 29-Apr-2016.
Corresponding Author:
Corresponding Author

Sawsan Taif

Department of Radiology, Khoula Hospital, PO Box 90, 116 Muscat, Sultanate of Oman.
E-mail: sawsantaif@gmail.com

Corresponding Author:
Corresponding Author

Sawsan Taif

Department of Radiology, Khoula Hospital, PO Box 90, 116 Muscat, Sultanate of Oman.
E-mail: sawsantaif@gmail.com

DOI: 10.4103/2156-7514.181492 Facebook Twitter Google Linkedin

ABSTRACT


Dermatofibrosarcoma protuberans (DFSP) is a rare soft tumor which originally represents a cutaneous sarcoma. It grows slowly and presents usually as nodular superficial lesion on the trunk or the extremities. Although these tumors are locally aggressive with high rate of recurrence following surgery; the prognosis is considered excellent when it is effectively treated. The radiological appearance of this tumor has rarely been studied and findings infrequently discussed in the literature probably because many lesions underwent resection before imaging. Although imaging is infrequently performed for this lesion; it can show characteristic features and demonstrate the full extent. Imaging may also play a role in the differentiation of this tumor from more serious soft tissue lesions such as more aggressive sarcomas and hemangioma. In this article, we discuss the imaging findings of DFSP that can aid in its diagnosis and its variable appearances. In addition; the clinical presentation and treatment options are also described with review of the previous literature.
Keywords: Dermatofibrosarcoma protuberans, literature review, low‑grade tumor, soft tissue sarcoma

Cited in 4 Documents

  1. Sami Kameel Saikaly and Amor Khachemoune (2017) A man with a large nodule on his lower leg. Journal of the American Academy of Physician Assistants 30(3):55. doi: 10.1097/01.JAA.0000512246.96989.53
  2. Alvaro E. Acosta and Catalina Santa Vélez (2017) Dermatofibrosarcoma Protuberans. Curr. Treat. Options in Oncol. 18(9):. doi: 10.1007/s11864-017-0498-5
  3. Simone Silva da Costa Aragão, Everson José dos Santos Leite, Alberto Eduardo Cox Cardoso and Ricardo Luiz Simões Houly (2018) An unusual variant of atrophic dermatofibrosarcoma protuberans. An. Bras. Dermatol. 93(2):282. doi: 10.1590/abd1806-4841.20187049
  4. Kamil Pohlodek, Iveta Mečiarová, Petr Grossmann and Zdeněk Kinkor (2017) Dermatofibrosarcoma protuberans of the breast: A case report. 14(1):993. doi: 10.3892/ol.2017.6206

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