Primary perivascular epithelioid cell tumor (PEComa) of the liver is a very rare tumor that originates from mesenchyma. Gastrointestinal tract with perivascular distribution is the most common anatomic sites of these tumors. Only few cases of hepatic PEComa have been described so far. Malignant PEComas exhibit aggressive behavior with poor prognosis, making early diagnosis crucial. Hereby, we report a 79-year-old female with unusually located mass in the liver. A partial curative hepatectomy has been done, and PEComa was diagnosed histopathologically. No evidence of recurrence was observed during the 6-month follow-up.
Isidro Machado, Ana Marhuenda, Marta Trallero, María Caballero, Jesús Santos, Julia Cruz and Rafael Estevan (2018) Angiomiolipoma epitelioide/PEComa hepático e hiperplasia nodular focal en una paciente con antecedentes de melanoma cutáneo. Revista Española de Patología:. doi: 10.1016/j.patol.2018.05.001
Pei Nie, Jie Wu, Hexiang Wang, Ruizhi Zhou, Lingling Sun, Jingjing Chen and Guangjie Yang (2019) Primary hepatic perivascular epithelioid cell tumors: imaging findings with histopathological correlation. Cancer Imaging19(1):. doi: 10.1186/s40644-019-0212-x
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